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BLOCH-SULZBERGER SYNDROME
Descriptors Found:
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DeCS
Descriptor
English
:
Incontinentia Pigmenti
Descriptor
Spanish
:
Incontinencia Pigmentaria
Descriptor
Portuguese
:
Incontinência Pigmentar
Synonyms
English
:
Bloch-Sulzberger Syndrome
Tree Number:
C16.131.077.445
C16.131.831.580
C16.320.850.420
C17.800.621.497
C17.800.804.580
C17.800.827.420
Definition
English
:
A genodermatosis occurring mostly in females and characterized by
skin
changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic.
Hyperpigmentation
is bizarre and irregular. Sixty percent of
patients
have abnormalities of eyes, teeth,
central nervous system
, and
skin
appendages.
Indexing Annotation
English
:
multiple
skin
& other abnorm; do not confuse with
INCONTINENTIA PIGMENTI
ACHROMIANS see
PIGMENTATION DISORDERS
History Note
English
:
91(87); was see under PIGMENTATION DISORDERS 1987-90
Allowable Qualifiers
English
:
blood
cerebrospinal fluid
chemically induced
classification
complications
diet therapy
diagnosis
drug therapy
economics
ethnology
embryology
enzymology
epidemiology
etiology
genetics
history
immunology
metabolism
microbiology
mortality
nursing
pathology
prevention & control
physiopathology
parasitology
psychology
radiography
rehabilitation
radionuclide imaging
radiotherapy
surgery
therapy
ultrastructure
urine
ultrasonography
veterinary
virology
Record Number:
19206
Unique Identifier:
D007184
Occurrence in VHL
:
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