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BULBAR PALSY, PROGRESSIVE
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DeCS
Descriptor
English
:
Bulbar Palsy, Progressive
Descriptor
Spanish
:
Parálisis Bulbar Progresiva
Descriptor
Portuguese
:
Paralisia Bulbar Progressiva
Synonyms
English
:
Paralysis, Bulbar
Fazio-Londe Syndrome
Tree Number:
C10.574.562.300
C10.668.460.300
Definition
English
:
A
motor neuron disease
marked by progressive weakness of the
muscles
innervated by
cranial nerves
of the lower
brain stem
. Clinical manifestations include
dysarthria
, dysphagia, facial weakness,
tongue
weakness, and fasciculations of the
tongue
and
facial muscles
. The
adult
form of the
disease
is marked initially by bulbar weakness which progresses to involve
motor neurons
throughout the neuroaxis. Eventually this condition may become indistinguishable from
AMYOTROPHIC LATERAL SCLEROSIS
. Fazio-Londe
syndrome
is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of
Neurology
, 6th ed, p1091;
Brain
1992 Dec;115(Pt 6):1889-1900)
History Note
English
:
2000(1966)
Allowable Qualifiers
English
:
blood
cerebrospinal fluid
chemically induced
classification
congenital
complications
diet therapy
diagnosis
drug therapy
economics
ethnology
embryology
enzymology
epidemiology
etiology
genetics
history
immunology
metabolism
microbiology
mortality
nursing
pathology
prevention & control
physiopathology
parasitology
psychology
radiography
rehabilitation
radionuclide imaging
radiotherapy
surgery
therapy
urine
ultrasonography
veterinary
virology
Record Number:
10433
Unique Identifier:
D010244
Occurrence in VHL
:
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