Search on: CHRISTMAS FACTOR 
Descriptors Found: 1
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Descriptor English:   Factor IX 
Descriptor Spanish:   Factor IX 
Descriptor Portuguese:   Fator IX 
Synonyms English:   Christmas Factor
Plasma Thromboplastin Component
PTC
Autoprothrombin II
Coagulation Factor IX  
Tree Number:   D12.776.124.125.375
D23.119.375
Definition English:   Storage-stable blood coagulation factor acting in the intrinsic pathway. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease). 
Entry Combination - descr/qualif English:   Factor IX/deficiency use Hemophilia B
 
See Related English:   Coagulants
 
Allowable Qualifiers English:  
administration & dosage adverse effects
agonists antagonists & inhibitors
analysis biosynthesis
cerebrospinal fluid chemistry
classification chemical synthesis
contraindications drug effects
diagnostic use economics
genetics history
immunology isolation & purification
metabolism pharmacology
physiology pharmacokinetics
poisoning radiation effects
supply & distribution secretion
standards toxicity
therapeutic use ultrastructure
urine  
Record Number:   22169 
Unique Identifier:   D005164 

Occurrence in VHL:
 

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