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COAGULATION FACTOR IX
Descriptors Found:
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DeCS
Descriptor
English
:
Factor IX
Descriptor
Spanish
:
Factor IX
Descriptor
Portuguese
:
Fator IX
Synonyms
English
:
Christmas Factor
Plasma Thromboplastin Component
PTC
Autoprothrombin II
Coagulation Factor IX
Tree Number:
D12.776.124.125.375
D23.119.375
Definition
English
:
Storage-stable
blood coagulation
factor acting in the intrinsic pathway. Its activated form, IXa,
forms
a complex with
factor VIII
and
calcium
on
platelet factor 3
to activate
factor X
to Xa. Deficiency of
factor IX
results in
HEMOPHILIA B
(Christmas Disease).
Entry Combination - descr/qualif
English
:
Factor IX
/
deficiency
use
Hemophilia B
See Related
English
:
Coagulants
Allowable Qualifiers
English
:
administration & dosage
adverse effects
agonists
antagonists & inhibitors
analysis
biosynthesis
cerebrospinal fluid
chemistry
classification
chemical synthesis
contraindications
drug effects
diagnostic use
economics
genetics
history
immunology
isolation & purification
metabolism
pharmacology
physiology
pharmacokinetics
poisoning
radiation effects
supply & distribution
secretion
standards
toxicity
therapeutic use
ultrastructure
urine
Record Number:
22169
Unique Identifier:
D005164
Occurrence in VHL
:
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