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DeCS
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Descriptor English:
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Ichthyosiform Erythroderma, Congenital
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Descriptor Spanish:
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Eritrodermia Ictiosiforme Congénita
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Descriptor Portuguese:
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Eritrodermia Ictiosiforme Congênita
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Synonyms English:
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Congenital Ichthyosiform Erythroderma
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Tree Number:
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C16.131.831.512.400
C16.320.850.400
C16.614.492.400
C17.800.428.333.250
C17.800.804.512.400
C17.800.827.400
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Definition English:
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Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type. |
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Indexing Annotation English:
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an ichthyosis rather than an erythroderma; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
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History Note English:
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91
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Allowable Qualifiers English:
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Record Number:
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28985
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Unique Identifier:
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D016113
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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