Search on: CYSTATHIONINE GAMMA-LYASE 
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Descriptor English:   Cystathionine gamma-Lyase 
Descriptor Spanish:   Cistationina gammaliasa 
Descriptor Portuguese:   Cistationina gama-Liase 
Synonyms English:   Cystathionase
Cysteine Desulfhydrase
Cystine Desulfhydrase
gamma-Cystathionase
Homoserine Deaminase
Homoserine Dehydratase  
Tree Number:   D08.811.520.300.250
Definition English:   A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1. 
Indexing Annotation English:   /defic: consider also CYSTATHIONINE /urine (IM) + AMINO ACID METABOLISM, INBORN ERRORS (IM)
History Note English:   91(75); was see under LYASES 1975-90 
Allowable Qualifiers English:  
administration & dosage adverse effects
antagonists & inhibitors analysis
biosynthesis blood
cerebrospinal fluid chemistry
classification chemical synthesis
contraindications drug effects
deficiency diagnostic use
economics genetics
history immunology
isolation & purification metabolism
pharmacology physiology
pharmacokinetics poisoning
radiation effects supply & distribution
secretion standards
toxicity therapeutic use
ultrastructure urine
Record Number:   3561 
Unique Identifier:   D003542 

Occurrence in VHL:
 

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