Search on: FACTOR XIII 
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Descriptor English:   Factor XIII 
Descriptor Spanish:   Factor XIII 
Descriptor Portuguese:   Fator XIII 
Synonyms English:   Coagulation Factor XIII
Factor XIII Transamidase
Fibrin Stabilizing Factor
Fibrinase
Laki-Lorand Factor  
Tree Number:   D12.776.124.125.475
D23.119.475
Definition English:   A fibrin-stabilizing plasma enzyme (TRANSGLUTAMINASES) that is activated by THROMBIN and CALCIUM to form FACTOR XIIIA. It is important for stabilizing the formation of the fibrin polymer (clot) which culminates the coagulation cascade. 
Indexing Annotation English:   activated form use FACTOR XIIIA
Entry Combination - descr/qualif English:   Factor XIII/deficiency use Factor XIII Deficiency
 
See Related English:   Coagulants
 
History Note English:   1970(1964); for FACTOR XIII TRANSAMIDASE see TRANSGLUTAMINASES (1990-2001) 
Allowable Qualifiers English:  
analogs & derivatives administration & dosage
adverse effects agonists
antagonists & inhibitors analysis
biosynthesis cerebrospinal fluid
chemistry classification
chemical synthesis contraindications
drug effects diagnostic use
economics genetics
history immunology
isolation & purification metabolism
pharmacology physiology
pharmacokinetics poisoning
radiation effects supply & distribution
secretion standards
toxicity therapeutic use
ultrastructure urine
Record Number:   22176 
Unique Identifier:   D005176 

Occurrence in VHL:
 

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