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DeCS
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Descriptor English:
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Hydranencephaly
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Descriptor Spanish:
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Hidranencefalia
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Descriptor Portuguese:
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Hidranencefalia
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Synonyms English:
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Cerebral Hemispheres, Absence, Congenital
Hemihydranencephaly
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Tree Number:
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C10.500.450
C16.131.666.450
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Definition English:
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A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307) |
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History Note English:
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91(64); was see under ANENCEPHALY 1979-90; was see under ANENCEPHALUS 1967-78
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Allowable Qualifiers English:
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Record Number:
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6984
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Unique Identifier:
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D006832
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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