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DeCS
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Descriptor English:
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Neuroectodermal Tumors, Primitive, Peripheral
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Descriptor Spanish:
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Tumores Neuroectodérmicos Periféricos Primitivos
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Descriptor Portuguese:
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Tumores Neuroectodérmicos Primitivos Periféricos
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Synonyms English:
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Neuroectodermal Tumor, Peripheral
Neuroepithelioma
Peripheral Primitive Neuroectodermal Tumors
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Tree Number:
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C04.557.465.625.600.590.650
C04.557.470.670.590.650
C04.557.580.625.600.590.650
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Definition English:
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A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with Ewing's Sarcoma (SARCOMA, EWING'S). They may arise from the chest wall, skin, orbit, kidney, and other structures and tend to be locally invasive or metastasize, although relatively benign forms may occur. Characteristic histologic features include a tendency to form Homer-Wright rosettes and to stain positively with neuron-specific enolase and vimentin. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2113; J Clin Oncol 1998 Mar;16(3):1150-7) |
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Indexing Annotation English:
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coord IM with precoord organ/neopl term (IM)
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See Related English:
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Sarcoma, Ewing's
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History Note English:
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2000(1994)
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Allowable Qualifiers English:
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Record Number:
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31258
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Unique Identifier:
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D018241
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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