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DeCS
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Descriptor English:
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Trihexosylceramides
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Descriptor Spanish:
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Trihexosilceramidos
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Descriptor Portuguese:
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Triexosilceramidas
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Synonyms English:
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Ceramide Trihexosides
Trihexosyl Ceramides
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Tree Number:
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D02.065.313.906
D09.400.410.420.525.200.906
D10.390.470.675.200.906
D10.570.877.360.612.200.906
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Definition English:
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Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (FABRY DISEASE). |
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Indexing Annotation English:
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/biosyn /physiol permitted
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History Note English:
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91(79); was see under GLYCOSPHINGOLIPIDS 1979-90
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Allowable Qualifiers English:
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Record Number:
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14680
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Unique Identifier:
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D014281
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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