Search on: GALACTOSYLCERAMIDES 
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Descriptor English:   Galactosylceramides 
Descriptor Spanish:   Galactosilceramidos 
Descriptor Portuguese:   Galactosilceramidas 
Synonyms English:   Galactocerebrosides
Galactosyl Ceramides  
Tree Number:   D02.065.313.250.450
D09.400.410.420.525.200.250.450
D10.390.470.675.200.250.450
D10.570.877.360.612.200.250.450
Definition English:   Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy. 
History Note English:   91(79); was see under CEREBROSIDES 1979-90 
Allowable Qualifiers English:  
administration & dosage adverse effects
agonists antagonists & inhibitors
analysis biosynthesis
blood cerebrospinal fluid
chemistry classification
chemical synthesis contraindications
deficiency diagnostic use
economics genetics
history immunology
isolation & purification metabolism
pharmacology physiology
pharmacokinetics poisoning
radiation effects supply & distribution
secretion standards
toxicity therapeutic use
urine  
Record Number:   5837 
Unique Identifier:   D005699 

Occurrence in VHL:
 

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