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DeCS
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Descriptor English:
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Ferrochelatase
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Descriptor Spanish:
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Ferroquelatasa
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Descriptor Portuguese:
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Ferroquelatase
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Synonyms English:
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Heme Synthetase
Porphyrin-Metal Chelatase
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Tree Number:
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D08.811.520.500
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Definition English:
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A mitochondrial enzyme found in a wide variety of cells and tissues. It is the final enzyme in the 8-enzyme biosynthetic pathway of HEME. Ferrochelatase catalyzes ferrous insertion into protoporphyrin IX to form protoheme or heme. Deficiency in this enzyme results in ERYTHROPOIETIC PROTOPORPHYRIA. |
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Entry Combination - descr/qualif English:
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Ferrochelatase/deficiency use Protoporphyria, Erythropoietic
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History Note English:
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91(77); was see under LYASES 1977-90
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Allowable Qualifiers English:
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Record Number:
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5403
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Unique Identifier:
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D005294
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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